Subcortical neurofibrillary degeneration presenting as steele‐richardson‐olszewski and other related syndromes: A review of 90 pathologically verified cases
Identifieur interne : 005A95 ( Main/Exploration ); précédent : 005A94; suivant : 005A96Subcortical neurofibrillary degeneration presenting as steele‐richardson‐olszewski and other related syndromes: A review of 90 pathologically verified cases
Auteurs : V. M. S. De Bruin [Royaume-Uni] ; Lees [Royaume-Uni]Source :
- Movement Disorders [ 0885-3185 ] ; 1994.
Descripteurs français
- Pascal (Inist)
- Wicri :
- topic : Homme.
English descriptors
- KwdEn :
- Aged, Aged, 80 and over, Akinesia, Brain (pathology), Cerebral Cortex (pathology), Dementia, Dentate nucleus, Exploration, Globus Pallidus (pathology), Human, Humans, Lewy body, Middle Aged, Nerve Degeneration (physiology), Neurofibrillary Tangles (pathology), Neurofibrillary tangles, Pathology, Pick body, Progressive, Review, Substantia Nigra (pathology), Supranuclear Palsy, Progressive (pathology), Supranuclear ophthalmoplegia, Supranuclear palsy, Thalamic Nuclei (pathology).
- MESH :
- pathology : Brain, Cerebral Cortex, Globus Pallidus, Neurofibrillary Tangles, Substantia Nigra, Supranuclear Palsy, Progressive, Thalamic Nuclei.
- physiology : Nerve Degeneration.
- Aged, Aged, 80 and over, Humans, Middle Aged.
Abstract
We have reviewed 90 patients from the literature with histopathological features compatible with currently accepted criteria for the diagnosis of the Steele‐Richardson‐Olszewski syndrome (SROS). Only 62 patients (69%) had clinically definite SROS based on the criteria of Maher and Lees. Neurofibillary degeneration of subcortical structures with involvement of the internal pallidum, the subthalamic nucleus, and substantia nigra was considered essential for the pathological diagnosis. Thirty‐six cases (40%) had neocortical neurofibrillary change that bore no clear relationship to the degree of cognitive impairment (χ2 = 9.293; p < 0.4107). Grumose degeneration of the dentate nucleus was present in 25 cases (28%), and occasionally there were other, less usual, findings such as Pick bodies and Lewy bodies.
Url:
DOI: 10.1002/mds.870090402
Affiliations:
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Le document en format XML
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Disord.</title><idno type="ISSN">0885-3185</idno><idno type="eISSN">1531-8257</idno><imprint><publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher><pubPlace>Hoboken</pubPlace><date type="published" when="1994">1994</date><biblScope unit="vol">9</biblScope><biblScope unit="issue">4</biblScope><biblScope unit="page" from="381">381</biblScope><biblScope unit="page" to="389">389</biblScope></imprint><idno type="ISSN">0885-3185</idno></series><idno type="istex">EFB7F5749F1E4DF3DC0D4A46D2EC44C2A7376ED6</idno><idno type="DOI">10.1002/mds.870090402</idno><idno type="ArticleID">MDS870090402</idno></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0885-3185</idno></seriesStmt></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Aged</term><term>Aged, 80 and over</term><term>Akinesia</term><term>Brain (pathology)</term><term>Cerebral Cortex (pathology)</term><term>Dementia</term><term>Dentate nucleus</term><term>Exploration</term><term>Globus Pallidus (pathology)</term><term>Human</term><term>Humans</term><term>Lewy body</term><term>Middle Aged</term><term>Nerve Degeneration (physiology)</term><term>Neurofibrillary Tangles (pathology)</term><term>Neurofibrillary tangles</term><term>Pathology</term><term>Pick body</term><term>Progressive</term><term>Review</term><term>Substantia Nigra (pathology)</term><term>Supranuclear Palsy, Progressive (pathology)</term><term>Supranuclear ophthalmoplegia</term><term>Supranuclear palsy</term><term>Thalamic Nuclei (pathology)</term></keywords><keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Brain</term><term>Cerebral Cortex</term><term>Globus Pallidus</term><term>Neurofibrillary Tangles</term><term>Substantia Nigra</term><term>Supranuclear Palsy, Progressive</term><term>Thalamic Nuclei</term></keywords><keywords scheme="MESH" qualifier="physiology" xml:lang="en"><term>Nerve Degeneration</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Aged</term><term>Aged, 80 and over</term><term>Humans</term><term>Middle Aged</term></keywords><keywords scheme="Pascal" xml:lang="fr"><term>Anatomopathologie</term><term>Article synthèse</term><term>Exploration</term><term>Homme</term><term>Ophtalmoplégie supranucléaire</term><term>Progressif</term></keywords><keywords scheme="Wicri" type="topic" xml:lang="fr"><term>Homme</term></keywords></textClass><langUsage><language ident="en">en</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">We have reviewed 90 patients from the literature with histopathological features compatible with currently accepted criteria for the diagnosis of the Steele‐Richardson‐Olszewski syndrome (SROS). Only 62 patients (69%) had clinically definite SROS based on the criteria of Maher and Lees. Neurofibillary degeneration of subcortical structures with involvement of the internal pallidum, the subthalamic nucleus, and substantia nigra was considered essential for the pathological diagnosis. Thirty‐six cases (40%) had neocortical neurofibrillary change that bore no clear relationship to the degree of cognitive impairment (χ2 = 9.293; p < 0.4107). Grumose degeneration of the dentate nucleus was present in 25 cases (28%), and occasionally there were other, less usual, findings such as Pick bodies and Lewy bodies.</div></front></TEI><affiliations><list><country><li>Royaume-Uni</li></country><region><li>Angleterre</li></region></list><tree><country name="Royaume-Uni"><region name="Angleterre"><name sortKey="De Bruin, V M S" sort="De Bruin, V M S" uniqKey="De Bruin V" first="V. M. S." last="De Bruin">V. M. S. De Bruin</name></region><name sortKey="Lees" sort="Lees" uniqKey="Lees" last="Lees">Lees</name></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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